1. Understanding of sequence of events leading to development of Pierre-Robin sequence and associated middle ear abnormalities based on discussion of embryology of facial and middle ear development.
2. Learning about range of middle ear abnormalities encountered in Pierre-Robin sequence.
3. Discussion of clinical correlation of observed imaging findings and brief discussion of severity and observed frequency of middle ear abnormalities.
Brief review of facial and middle ear embryology.
Imaging of classic triad in Pierre-Robin sequence:
- micrognathia-rethrognatia,
- glossoptosis
- Cleft palate.
Imaging of commonly occurring middle ear abnormalities in Pierre-Robin sequence:
- Ottitis media
- Auricular anomalies
- Artesia of external auditory canal
- Dysplastic/aplastic changes of the ossicles
- Aplasia of semicircular canals
- Large vestibular aqueduct
- Dehiscence of fallopian tube.
Correlation of middle ear abnormalities with other manifestation of Pierre-Robin syndrome
Haroyan, H,
Ginat, D,
Abnormalities of Middle Ear in Pierre-Robin Sequence. Radiological Society of North America 2014 Scientific Assembly and Annual Meeting, - ,Chicago IL.
http://archive.rsna.org/2014/14018076.html
