Maira Sarpi MD, Presenter: Nothing to Disclose

Regina Lucia Elia Gomes MD, Abstract Co-Author: Nothing to Disclose

Marcio Ricardo Taveira Garcia MD, Abstract Co-Author: Nothing to Disclose

Flavia I. Cevasco MD, Abstract Co-Author: Nothing to Disclose

Mauro Miguel Daniel MD, Abstract Co-Author: Nothing to Disclose

Eloisa Maria Santiago Gebrim MD, Abstract Co-Author: Nothing to Disclose

Literature review emphasizing head and neck manifestations of IgG4-related diseasethis (a newly recognized clinical condition). To highight and exemplify possible imaging features and follow up findings using clinical cases. To aggregate this differential diagnosis in the evaluation of head and neck tumors. 

IgG4-related disease has been recently recognized as an inflammatory condition, characterized by pseudotumoral lesions and particular histopathological findings. Recently the occurrence in diverse organs was linked, so previously recognized head and neck distinct lesions are now acknowledged as manifestations of this disease (inflammatory pseudotumors, Küttner’s tumor, Mikulicz’s syndrome, Riedel’s thyroiditis, etc). In some patients it manifests in a single structure, and the differential diagnosis with tumors is important. Initially imaging features do not permit this distinction, but when clinical and histopathological data directs to an IgG4-related disease, imaging follow up demonstrates a characteristic significative response to treatment with glucocorticoids.  Cases selected from our digital archive will demonstrate the manifestations in diverse head and neck structures (ptuitary gland, skull base, paransal sinuses, parotid gland, parapharyngeal space and lymph nodes) and follow-up imaging findings .  

http://abstract.rsna.org/uploads/2014/14015948/14015948_emvw.pdf

Sarpi, M, Gomes, R, Garcia, M, Cevasco, F, Daniel, M, Gebrim, E, Head and Neck Lesions in IgG4-related Disease - A Newly Recognized Systemic Inflammatory Condition .  Radiological Society of North America 2014 Scientific Assembly and Annual Meeting, - ,Chicago IL. http://archive.rsna.org/2014/14015948.html