Kiran Mahadev Sargar MBBS, MD, Presenter: Nothing to Disclose

Geetika Khanna MD, MS, Abstract Co-Author: Nothing to Disclose

Elizabeth Fowler Sheybani MD, Abstract Co-Author: Nothing to Disclose

Fibroblastic-myofibroblastic tumors account for about 12% of pediatric soft tissue tumors.Though most are benign, they can be locally aggressive and occasionally malignant. Most fibrous tumors have low signal intensity on T1 images, and variable signal on T2 weighted images depending on stage of proliferation. Diagnosis of Gardner fibroma may represent initial presentation of underlying familial adenomatous polyposis syndrome. Desmoid fibromatoses is locally aggressive neoplasm that has tendency to recur locally without evidence of metastatic spread. It has association with Gardner syndrome. Juvenile nasopharyngeal angiofibroma is a benign tumor that appears as an intensely enhancing mass along the pterygomaxillary fissure. Infantile fibrosarcoma tend to have multiple flow voids on MRI and can mimic hemangiomas and kaposiform hemangioendothelioma.

1. WHO classification of pediatric fibrous tumors - A.Pseudosarcomas (Nodular fasciitis) B.Fibromas (Gardner fibroma) C.Fibromatoses (Infantile myofibroma,Fibromatosis colli,Nasopharyngeal angiofibroma) D.Intermediate tumors (Desmoid,Inflammatory myofibroblastic tumor,Lipofibromatosis,Infantile fibrosarcoma) E.Sarcomas (Low grade fibromyxoid sarcoma)   2. We will discuss clinical,pathologic and imaging features of these common pediatric fibrous tumors. 

http://abstract.rsna.org/uploads/2014/14008039/14008039_pm3l.pdf

Sargar, K, Khanna, G, Sheybani, E, Fibroblastic and Myofibroblastic Tumors of Childhood and Adolescence.  Radiological Society of North America 2014 Scientific Assembly and Annual Meeting, - ,Chicago IL. http://archive.rsna.org/2014/14008039.html