Thomas Robert Semple MBBS, BSC, Presenter: Nothing to Disclose

Catherine Mary Owens MD, Abstract Co-Author: Nothing to Disclose

Michael Ashworth, Abstract Co-Author: Nothing to Disclose

The purpose of this exibit is to: Review and update the classification of childhood interstitial lung diseases (ChILD), introducing the new and important added conditions of pleuroparenchymal fibroelastosis and Filamin A protein deficiency Demonstrate and introduce the HRCT features of these conditions with cases from our institution, with histological correlation

Introduction Review of Classification -   Infantile ChILD - Developmental disorders, Lung growth disorders, Surfactant dysfunction and undefined (NEHI and PIG) Childhood ChILD - Normal host, Immunocompromised host, Systemic disorders New-comers - Pleuroparenchymal fibroelastosis (PPFE) and Filamin A protein (FLNA) deficiency Imaging features and histopathologic correlation - Infant ChILD Developmental disorders (including ACD/MPV) Lung growth disorders (including CAD) Surfactant dysfunction Undefined aetiology (NEHI and PIG) New-comers (FLNA) Childhood ChILD Normal host (including constrictive bronchiolitis and NSIP) Immunocompromised (including LIP) Systemic diseases (including LCH) Mimics of ChILD The role of the radiologist Summary  

http://abstract.rsna.org/uploads/2014/14007812/14007812_asv7.pdf

Semple, T, Owens, C, Ashworth, M, The New Kids on the Block: Childhood Interstitial Lung Disease (ChILD) Classification in 2014 - Introducing the two recent additions: Pleuroparenchymal Fibroelastosis and Filamin A Protein Deficiency.  Radiological Society of North America 2014 Scientific Assembly and Annual Meeting, - ,Chicago IL. http://archive.rsna.org/2014/14007812.html