Carlos Marin MD, Presenter: Nothing to Disclose

Angel Lancharro MD, Abstract Co-Author: Nothing to Disclose

Yolanda Ruiz MD, Abstract Co-Author: Nothing to Disclose

Alejandro Rodriguez MD, Abstract Co-Author: Nothing to Disclose

Enrique Maroto, Abstract Co-Author: Nothing to Disclose

The purpose of this exhibit is: 1. To review the definitions of cardiac position, visceroatrial situs, heterotaxy and isomerism. 2. To describe the segmental approach to the Cardiac Magnetic Resonance (CMR) of cardiac malpositions and heterotaxy syndromes. 3. To discuss the associations between situs abnormalitlies and venous, ventricular, conotruncal and arterial anomalies. 4. To show the CMR protocol for a comprehensive evaluation of heterotaxy syndromes.

Cardiac malpositions are estimated to occur in 0.1/1000 live births, and heterotaxy syndromes affect 0,8% of patients with congenital heart disease. A comprehensive imaging examination is mandatory to guide the appropriate medical management and surgical correction. Systematic segmental approach must be used, including abdominal viscera, lungs, atria, ventricles and great vessels. Certain associations exist between isomerisms and cardiac segment malformations, albeit a great diversity of combinations has been reported. Treatment choices for these patients vary from medical follow up to complex surgical procedures, including systemic-to-pulmonary palliative surgery, such as Kawashima or Fontan procedure. To accomplish a comprehensive MR examination, morphologic and functional data should be included in the radiology report.

http://abstract.rsna.org/uploads/2014/14003879/14003879_3v38.pdf

Marin, C, Lancharro, A, Ruiz, Y, Rodriguez, A, Maroto, E, Puzzling Hearts: Magnetic Resonance Imaging in Cardiac Malpositions and Heterotaxy Syndromes.  Radiological Society of North America 2014 Scientific Assembly and Annual Meeting, - ,Chicago IL. http://archive.rsna.org/2014/14003879.html