Lan-Chau Thi Kha MD, MSc, Presenter: Nothing to Disclose

David M Hwang MD,PhD, Abstract Co-Author: Nothing to Disclose

Demetris Andrea Patsios MBBCh, Abstract Co-Author: Nothing to Disclose

Gordon Weisbrod MD, Abstract Co-Author: Nothing to Disclose

Taebong Chung MD, Abstract Co-Author: Nothing to Disclose

Pleuroparenchymal fibroelastosis (PPFE) has recently been classified as a separate interstitial pneumonia. PPFE may be idiopathic or may be related to underlying medical conditions such as bone marrow and lung transplantation, recurrent infection and autoimmunity. An understanding of the etiologies, histopathology and imaging characteristics of this rare interstitial pneumonia is important, particularly as the radiologist may be the first member of the health care team to consider this diagnosis in the presenting patient. The purpose of the exhibit is: 1. To review the etiologies, clinical presentation and demographic of PPFE. 2. To review the underlying histopathologic changes that produces the chest radiograph and CT imaging appearances of PPFE. Histopathologic imaging with correlative radiographic imaging from our institution will be used as teaching cases. 3. To highlight the characteristic findings of PPFE on chest radiograph and CT. Idiopathic, bone marrow transplant and lung transplant cases of PPFE from our institution will be used to illustrate specific imaging features. Imaging of progressive PPFE will also be presented.

1. Demographics and clinical presentation 2. Etiologies of PPFE 3. Imaging-histopathologic correlation of PPFE: 4. Imaging characteristics of PPFE on: • chest radiograph • chest CT

http://abstract.rsna.org/uploads/2014/14003147/14003147_aq9m.pdf

Kha, L, Hwang, D, Patsios, D, Weisbrod, G, Chung, T, Imaging Characteristics of Pleuroparenchymal Fibroelastosis, A Rare form of Interstitial Pneumonia: What the Radiologist Needs to Know.  Radiological Society of North America 2014 Scientific Assembly and Annual Meeting, - ,Chicago IL. http://archive.rsna.org/2014/14003147.html