Jose Luis Vercher-Conejero MD, Presenter: Nothing to Disclose

Laura Pelegri-Martinez MD, Abstract Co-Author: Nothing to Disclose

Cristina Ruiz-Llorca, Abstract Co-Author: Nothing to Disclose

Jose L Loaiza, Abstract Co-Author: Nothing to Disclose

Consuelo Olivas, Abstract Co-Author: Nothing to Disclose

Antonio Mateo, Abstract Co-Author: Nothing to Disclose

Pilar Bello-Arques, Abstract Co-Author: Nothing to Disclose

Isabel Hervas, Abstract Co-Author: Nothing to Disclose

Rosa Perez-Velasco, Abstract Co-Author: Nothing to Disclose

Antonio Rivas, Abstract Co-Author: Nothing to Disclose

To evaluate the usefulness of the lymphoscintigraphy in patients younger than 20 years-old with congenital malformations presenting swelling..

Over the past three years, we studied 19 patients aged between 9 months and 20 years-old, who had congenital pathology and associated oedema on a limb and / or face, reason why we made the lymphoscintigraphy. The patient group comprised: 1 Noonan syndrome, 9 Familiar Lymphedema, 2 Prader-Willi syndromes (PW), and 1 Turner Syndrome, all of them with involvement of the lower limbs (LL); 3 Klippel - Trenaunay Syndromes (KT) with involvement of the LL, upper limbs (UL), and one of them also in the face; and 3 Lymphatic Dysplasias with oedema in UL and in LL. Four doses of 11.1 MBq (0.3 mCi) of Technetium-99m- albumin nanocolloid were injected subcutaneously, between the toes into the swollen limb, into the interdigital web spaces on the patient's right and left lower (or upper) extremities, and in the case of the face we administered a dose on the online facial half. A passive muscular exercise was recommended in order to reduce the variability of lymphatic function. We performed a body scan 20 and 180 minutes after injection.  

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Lymphedema is a condition that is often associated with multiple syndromes. The use of lymphoscintigraphy has proved reliable and reproducible, and may be useful in the study of lymphatic drainage in patients with oedema and associated malformations, which wants to discard abnormality in the lymphatic system. Our findings helped confirm the clinical diagnosis and thereby customize treatment.  

The lymphoscintigraphy has proved reliable and reproducible, and may be useful in the study of lymphatic drainage in patients with oedema and associated malformations.

Vercher-Conejero, J, Pelegri-Martinez, L, Ruiz-Llorca, C, Loaiza, J, Olivas, C, Mateo, A, Bello-Arques, P, Hervas, I, Perez-Velasco, R, Rivas, A, Lymphoscintigraphy as a Useful Method in the Study of Young Patients with Oedemas and Congenital Pathology Associated Malformations.  Radiological Society of North America 2009 Scientific Assembly and Annual Meeting, November 29 - December 4, 2009 ,Chicago IL. http://archive.rsna.org/2009/8016971.html