Jeremy Neuman MD, Abstract Co-Author: Nothing to Disclose

Joseph Platnick MD, Presenter: Nothing to Disclose

Gary Giangola, Abstract Co-Author: Nothing to Disclose

Krista Frasier, Abstract Co-Author: Nothing to Disclose

Jonathan Scheiner, Abstract Co-Author: Nothing to Disclose

1) Review the historical, clinical and therapeutic aspects of Klippel Trenaunay (KTS) and Parks Weber syndrome 2) Present clinical and ultrasonographic findings which are suspicious for an underlying arteriovenous connection in KTS 3) Demonstrate the MR angiographic findings of AV connections in Parks Weber patients, and its impact on therapy

1) Definition, historical context and clinical features 2) Clinical and ultrasonographic findings suspicious for underlying AV connection in KTS patients, including: AV connection on US, arterial waveforms, pain and heat around knee after exercise, foot varicosities 3) MR angiographic examples of Parks Weber as definitive evaluations for an underlying AV connection 4) Relevance of the AVM in treatment planning, specifically to radiofrequency ablation of the varicose veins  

KT is a syndrome characterized by presence of two of the following features: capillary malformation, soft tissue or bone hypertrophy and venous malformations. It is referred to as PW syndrome when found in association with an AVM. Our practice has defined clinical and ultrasonographic findings suspicious for underlying AV connection. However, due to occult AVMs, we recommend all KTS patients have MRA, as the presence of an AVM may alters the approach to therapy.  

Neuman, J, Platnick, J, Giangola, G, Frasier, K, Scheiner, J, MR Angiography of Klippel Trenaunay Syndrome: To Image or Not to Image, That Is the Question.  Radiological Society of North America 2009 Scientific Assembly and Annual Meeting, November 29 - December 4, 2009 ,Chicago IL. http://archive.rsna.org/2009/8008153.html